totalis is a very rare autosomal recessive entity (Piryani et al, 2007).
Aim was to give an overview of the literature on left-sided acute appendicitis (LSAA) associated with situs inversus
totalis (SIT) and midgut malrotation (MM).
(3), the incidence of appendicitis with left lower quadrant pain was reported as 0.04%, and 0.024% of cases were associated with malrotation of the intraabdominal organs and 0.016% with situs inversus
totalis may be observed together with bronchitis, sinusitis, congenital heart diseases, and biliary atresia.
USG upper abdomen showed the evidence of situs inversus
totalis with spleen on right side and liver on left side.
Talking about the challenges faced by a surgeon in the clinical setting of undiagnosed situs inversus
, Dr Ananth Pai Kalsank, specialist in general surgery at NMC Specialty Hospital, Abu Dhabi, said: "In a typical ER room situation where time is the key, if a patient reports an acute pain in the left hand side, we suspect the colon or kidney.
With situs solitus and situs inversus
, the atrial situs always corresponds to the visceral situs; with situs ambiguous, the arrangement of the organs is not as ordered, and the relation between the atria and the viscera is inconsistent [1, 2, 4].
"However, while people with situs inversus
have their heart beating on the right, my heart still beats on the left, so I'm even more of an anomaly."
Out of 307 operated patients, 4 (1.3%) patients had previous modified Blalock Taussig shunts, 2 (0.6%) associated ASD with TOF, 3 (0.9%) had co-association of PDA, 2 (0.6%) large conal arterial branch crossing at the annulus, 3 (0.9%) dextrocardia with situs inversus
, 12(3.9%) TOF with double outlet right ventricle (DORV), 2 (0.6%) with associated complete AV canal defect, 8 (2.60%) with absent pulmonary valve syndrome, 15 (5.5%) with left pulmonary artery stenosis.
, the complete mirror-image reversal of the organs, is very rare, with a prevalence of 1/20 000.
Keywords: Polysplenia syndrome, situs inversus
totalis, pancreas, pancreatic hypoplasia
In this report, we discuss an interesting case of an infant who presented with a seizure after birth and was later found to have panhypopituitarism with an absence of pituitary gland, situs inversus
, and left ureterocele with hydronephrosis.