Inadequate ossification of the contours of the embryonic vertebral arch may lead to spinal deformities such as spina bifida, scoliosis, kyphosis/kyphoscoliosis, hemivertebra
and posterior wedging of vertebrae, and cervical ribs, and these conditions may be seen together with the absence of the posterior thoracic vertebral arch or syringomyelia [10, 21, 24].
The efficacy and complications of posterior hemivertebra
The aim of this study was to present the results of average period of five-year follow-up in patients, diagnosed with congenital scoliosis and kyphoscoliosis and treated with transpedicular instrumentation and fusion methods after hemivertebra
resection with the posterior approach.
Normal 10.14% Hydrocephalus/ventriculomegaly 25.36% Chiari malformation 3.4% Dandy-Walker malformation 5.7% Holoprosencephaly 2.3% Intracranial masses Cysts 3.4% Microcephaly 1.1% Corpus callosum agenesis 6.9% Nonspecific 2.3% Soft-tissue masses 2.3% Hemivertebra
1.1% Diaphragmatic hernia 1.1% Cardiac rhabdomyoma 1.1 Pulmonary sequestration 1.1 Note: Table made from pie chart.
Congenital scoliosis is a lateral curvature of the spine associated with vertebral anomalies such as block vertebra, wedge vertebra, single hemivertebra
, two unilateral hemivertebrae, a unilateral unsegmented bar, or a unilateral unsegmented bar with contralateral hemivertebrae at the same level.
Skeletal radiography showed sacral agenesis and hemivertebra
. Fibula, bones of foot and digits were absent (Fig.2).
(3) En el estudio retrospectivo transversal realizado por Avila y sus colegas en 8 pacientes con asociacion VACTERL reportaron que el 100% tenian cardiopatia congenita (CIA, CIV), el 75% defectos vertebrales: hemivertebra
y fusion vertebral.
Terminated cases, because of associated severe / lethal extra-cardiac pathologies (Group A) Pathological classification n = 39 Clinical diagnosis (n) Chromosomal pathologies 23 Trisomy 21 (n=13), trisomy 18 (n=8), trisomy 13 (n=2) Genitourinary pathologies 6 Bilateral renal agenesis (n=2), multicystic dysplastic kidneys associated with oligo- / anhydramnios (n=4) Central nervous system 7 Anencephaly (n=1), pathologies holoprosencephaly (n=2), hemivertebra
(n=l), vermis agenesis (n=1), neural tube defect (n=2) Other 3 Severe generalized hydrops / septated cystic hygroma (n=3) Table 3.
Servikal grafide tum servikal vertebralari iceren yapisal anomaliler (hemivertebra
, kelebek vertebra ve blok vertebra) izlendi (Resim 3).